Broadening The Imaging Phenotype of Dysferlinopathy at Different Disease Stages
Díaz J, Woudt L, Suazo L, Garrido C, Caviedes P, Cardenas AM, Castiglioni C, Bevilacqua JA.
Muscle Nerve. 2016. 54(2):203-10.
The study aimed at describes MRI of dysferlinopathy and to correlate it with objective measures of motor dysfunction.
MRI infiltration score correlated positively with disease duration and negatively with MFM scale.
Keywords: Clinical trials, MRI, Muscle disease, Whole-body MRI, dysferlinopathy, motor function measure
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