Upper limb strength and function changes during a one-year follow-up in non-ambulant patients with Duchenne Muscular Dystrophy: an observational multicenter trial
Seferian AM, Moraux A, Annoussamy M, Canal A, Decostre V, Diebate O, Le Moing AG, Gidaro T, Deconinck N, Van Parys F, Vereecke W, Wittevrongel S, Mayer M, Maincent K, Desguerre I, Thémar-Noël C, Cuisset JM, Tiffreau V, Denis S, Jousten V, Quijano-Roy S, Voit T, Hogrel JY, Servais L.
PLoS One. 2015. 10(2): e0113999.
Results of a multicenter study using specifically designed tools to assess grip, pinch strength, and hand function in wheelchair-bound patients in 53 non-ambulant patients with Duchenne muscular dystrophy aged 9-28 years. MFM was also performed at baseline and 6 and 12 months later.
Results showed that function is directly correlated with strength as measured by the MyoSet and MFM-D3 score.
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