Reduced mandibular range of motion in Duchenne Muscular Dystrophy: predictive factors
van Bruggen HW, Van Den Engel-Hoek L, Steenks MH, Bronkhorst EM, Creugers NH, de Groot IJ, Kalaykova SI.
J Oral Rehabil. 2015. 42(6):430-8.
Objectives were to determine whether the mandibular range of motion in Duchenne Muscular Dystrophy (DMD) is impaired and to explore predictive factors for the active maximum mouth opening (aMMO).
Based on the ambulatory function and MFM scores, patients were divided into4 groups, from early and late ambulatory stage to late non-ambulatory stage with upper limb function and postural maintenance increasingly limited.
All mandibular movements were reduced in all patient groups compared to the healthy controls. A positive correlation is found between aMMO and the body height or disease progression, with MFM total score as the strongest independent risk factor.
Keywords: Duchenne muscular dystrophy, masticatory system, mandibular range of motion, quantitative ultrasound, masticatory muscles, MFM
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