Dysphagia in spinal muscular atrophy type II: More than a bulbar problem?
van den Engel-Hoek L, Erasmus CE, van Bruggen HW, de Swart BJM, Sie LTL, Steenks MH, de Groot IJ.
Neurology 2009. 73: 1787-1791.
Swallowing liquid and solid food from 6 children with SMA type II and 6 healthy children from 6 to 13 years was studied using surface EMG of the submental muscle group and a video fluoroscopic swallow study (VFSS). The MFM was used to assess the sitting position, the arm function and head and neck control in SMA patients.
Keywords: Spinal muscular atrophy, feeding problems, dysphagia, video fluoroscopic swallow
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